| CASE REPORT |
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| Year : 2017 | Volume
: 9
| Issue : 1 | Page : 73-77 |
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Marfan syndrome
T Sivasankari1, Philips Mathew2, Ravi David Austin3, Sakthi Devi4
1 Department of Oral Medicine and Radiology, Indira Gandhi Institute of Dental Sciences, Sri Balaji Vidyapeeth University, Puducherry, India
2 Department of Oral Medicine and Radiology, Government Dental College, Kottayam, Kerala, India
3 Department of Oral Medicine and Radiology, Rajah Muthiah Dental College, Chidambaram, Tamil Nadu, India
4 Department of Periodontology, Indira Gandhi Institute of Dental Sciences, Sri Balaji Vidyapeeth University, Puducherry, India
Correspondence Address:
T Sivasankari
Indira Gandhi Institute of Dental Sciences, Sri Balaji Vidyapeeth University, Pondicherry - 607 402
India
 Source of Support: None, Conflict of Interest: None  | Check |
DOI: 10.4103/jpbs.JPBS_326_16
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Marfan syndrome (MFS) is the autosomal dominant-inherited multisystem connective-tissue disorder, with a reported incidence of 1 in 10,000 individuals and equal distribution in both genders. The main clinical manifestation of this disorder consists of an exaggerated length of the upper and lower limbs, hyperlaxity, scoliosis, alterations in the cardiovascular and pulmonary systems, and atypical bone overgrowth. Orofacial manifestations such as high-arched palate, hypodontia, long narrow teeth, bifid uvula, mandibular prognathism, and temporomandibular disorders are also common. Early diagnosis of MFS is essential to prevent the cardiovascular complications and treatment of orofacial manifestations, thus to increase the quality of life of the patient. |
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