Journal of Pharmacy And Bioallied Sciences

CYTOLOGY SECTION - CASE REPORT
Year
: 2012  |  Volume : 4  |  Issue : 6  |  Page : 349--352

Sturge-Weber syndrome


Natarajan Manivannan1, Subramanium Gokulanathan1, Ramakrishnan Swamy Ahathya2, Gubernath3, Rajkumar Daniel2, Shanmugasundaram2 
1 Department of Oral and Maxillofacial Surgery, Vivekanandha Dental College for Women, Tiruchengode, India
2 Department of Periodontology and Implantology, Vivekanandha Dental College for Women, Tiruchengode, India
3 Department of Periodontology and Implantology, Meenakshi Ammal Dental College, Chennai, Tamil Nadu, India

Correspondence Address:
Natarajan Manivannan
Department of Oral and Maxillofacial Surgery, Vivekanandha Dental College for Women, Tiruchengode
India

Encephalotrigeminal angiomatosis (Sturge-Weber syndrome) is a rather uncommon congenital condition characterized by the combination of venous angioma of the leptomeninges over the cerebral cortex with ipsilateral angiomatous lesions of the face, and sometimes the skull, jaws, and oral soft tissues. A case of portwine stain with intraoral gingival hemangioma is presented. There were no other systemic manifestations. Patient reported with a complaint of localized tumor-like swelling in gums. Based on the presence of sharply demarcated vascular lesion unilaterally on the face and with ipsilateral intraoral vascular hyperplasia in the lip and gingiva, a variant of encephalotrigeminal angiomatosis was diagnosed. Ultrasound Doppler flowmetry was used to determine the blood flow. Dental management included plaque control instructions, scaling, root planning, and excision of the lesion done under general anesthesia. Close follow-up and meticulous plaque control have kept the oral condition under fairly good control.


How to cite this article:
Manivannan N, Gokulanathan S, Ahathya RS, Gubernath, Daniel R, Shanmugasundaram. Sturge-Weber syndrome.J Pharm Bioall Sci 2012;4:349-352


How to cite this URL:
Manivannan N, Gokulanathan S, Ahathya RS, Gubernath, Daniel R, Shanmugasundaram. Sturge-Weber syndrome. J Pharm Bioall Sci [serial online] 2012 [cited 2021 Sep 26 ];4:349-352
Available from: https://www.jpbsonline.org/article.asp?issn=0975-7406;year=2012;volume=4;issue=6;spage=349;epage=352;aulast=Manivannan;type=0